{"id":2198,"date":"2021-09-14T10:43:05","date_gmt":"2021-09-14T08:43:05","guid":{"rendered":"http:\/\/bluter.at\/wp\/?page_id=2198"},"modified":"2024-12-30T13:25:42","modified_gmt":"2024-12-30T12:25:42","slug":"von-willebrand-syndrom","status":"publish","type":"page","link":"https:\/\/bluter.at\/wp\/von-willebrand-syndrom\/","title":{"rendered":"Von-Willebrand-Syndrom"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"2198\" class=\"elementor elementor-2198\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-3262fe1f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"3262fe1f\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-20 elementor-top-column elementor-element elementor-element-302a1577\" data-id=\"302a1577\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-20 elementor-top-column elementor-element elementor-element-4f8e86ec\" data-id=\"4f8e86ec\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d211133 elementor-widget elementor-widget-theme-site-logo elementor-widget-image\" data-id=\"d211133\" data-element_type=\"widget\" data-widget_type=\"theme-site-logo.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<a href=\"https:\/\/bluter.at\/wp\">\n\t\t\t\t\t\t\t<img decoding=\"async\" width=\"160\" height=\"160\" src=\"https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1-160x160.png\" class=\"attachment-thumbnail size-thumbnail wp-image-6739\" alt=\"\" srcset=\"https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1-160x160.png 160w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1-270x270.png 270w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1-192x192.png 192w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1-180x180.png 180w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1-32x32.png 32w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2021\/03\/cropped-cropped-cropped-cropped-cropped-OeHG-Logo-Schriftzug_web-transparent-1-1.png 512w\" sizes=\"(max-width: 160px) 100vw, 160px\" \/>\t\t\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-20 elementor-top-column elementor-element elementor-element-f86d37d\" data-id=\"f86d37d\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-20 elementor-top-column elementor-element elementor-element-59c28107\" data-id=\"59c28107\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a5d267f elementor-search-form--skin-classic elementor-search-form--button-type-icon elementor-search-form--icon-search elementor-widget elementor-widget-search-form\" data-id=\"a5d267f\" data-element_type=\"widget\" data-settings=\"{&quot;skin&quot;:&quot;classic&quot;}\" data-widget_type=\"search-form.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<form class=\"elementor-search-form\" role=\"search\" action=\"https:\/\/bluter.at\/wp\" method=\"get\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-search-form__container\">\n\t\t\t\t\t\t\t\t<input placeholder=\"Suche...\" class=\"elementor-search-form__input\" type=\"search\" name=\"s\" title=\"Search\" value=\"\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t<button class=\"elementor-search-form__submit\" type=\"submit\" title=\"Search\" aria-label=\"Search\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t<i aria-hidden=\"true\" class=\"fas fa-search\"><\/i>\t\t\t\t\t\t\t<span class=\"elementor-screen-only\">Search<\/span>\n\t\t\t\t\t\t\t\t\t\t\t<\/button>\n\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t<\/form>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-aea3ee8 elementor-shape-square e-grid-align-right elementor-grid-0 elementor-widget elementor-widget-global elementor-global-8364 elementor-widget-social-icons\" data-id=\"aea3ee8\" data-element_type=\"widget\" data-widget_type=\"social-icons.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-social-icons-wrapper elementor-grid\">\n\t\t\t\t\t\t\t<span class=\"elementor-grid-item\">\n\t\t\t\t\t<a class=\"elementor-icon elementor-social-icon elementor-social-icon-envelope elementor-animation-bounce-in elementor-repeater-item-b8cf904\" href=\"https:\/\/bluter.at\/wp\/newsletter\/\">\n\t\t\t\t\t\t<span class=\"elementor-screen-only\">Envelope<\/span>\n\t\t\t\t\t\t<i class=\"fas fa-envelope\"><\/i>\t\t\t\t\t<\/a>\n\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<span class=\"elementor-grid-item\">\n\t\t\t\t\t<a class=\"elementor-icon elementor-social-icon elementor-social-icon-facebook elementor-animation-bounce-in elementor-repeater-item-b31a03c\" href=\"https:\/\/www.facebook.com\/oehges\/\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-screen-only\">Facebook<\/span>\n\t\t\t\t\t\t<i class=\"fab fa-facebook\"><\/i>\t\t\t\t\t<\/a>\n\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<span class=\"elementor-grid-item\">\n\t\t\t\t\t<a class=\"elementor-icon elementor-social-icon elementor-social-icon-instagram elementor-animation-bounce-in elementor-repeater-item-37f4f84\" href=\"https:\/\/www.instagram.com\/oehges\/?fbclid=IwAR0C3Rj7zq33m3Do4Zx5666_PZr6oBittbVG74Z56PxgJPHbBwy5GIQoZK0\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-screen-only\">Instagram<\/span>\n\t\t\t\t\t\t<i class=\"fab fa-instagram\"><\/i>\t\t\t\t\t<\/a>\n\t\t\t\t<\/span>\n\t\t\t\t\t\t\t<span class=\"elementor-grid-item\">\n\t\t\t\t\t<a class=\"elementor-icon elementor-social-icon elementor-social-icon-youtube elementor-animation-bounce-in elementor-repeater-item-59fd92e\" href=\"https:\/\/www.youtube.com\/user\/BluterAustria\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-screen-only\">Youtube<\/span>\n\t\t\t\t\t\t<i class=\"fab fa-youtube\"><\/i>\t\t\t\t\t<\/a>\n\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-20 elementor-top-column elementor-element elementor-element-2696dc97\" data-id=\"2696dc97\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-37d32e28 elementor-section-full_width elementor-section-height-default elementor-section-height-default\" data-id=\"37d32e28\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-766401fa\" data-id=\"766401fa\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-66c0f1d1 elementor-nav-menu__align-center elementor-nav-menu--dropdown-tablet elementor-nav-menu__text-align-aside elementor-nav-menu--toggle elementor-nav-menu--burger elementor-widget elementor-widget-nav-menu\" data-id=\"66c0f1d1\" data-element_type=\"widget\" data-settings=\"{&quot;sticky&quot;:&quot;top&quot;,&quot;submenu_icon&quot;:{&quot;value&quot;:&quot;&lt;i class=\\&quot;fas fa-chevron-down\\&quot;&gt;&lt;\\\/i&gt;&quot;,&quot;library&quot;:&quot;fa-solid&quot;},&quot;layout&quot;:&quot;horizontal&quot;,&quot;toggle&quot;:&quot;burger&quot;,&quot;sticky_on&quot;:[&quot;desktop&quot;,&quot;tablet&quot;,&quot;mobile&quot;],&quot;sticky_offset&quot;:0,&quot;sticky_effects_offset&quot;:0}\" data-widget_type=\"nav-menu.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t<nav migration_allowed=\"1\" migrated=\"0\" role=\"navigation\" class=\"elementor-nav-menu--main elementor-nav-menu__container elementor-nav-menu--layout-horizontal e--pointer-underline e--animation-fade\">\n\t\t\t\t<ul id=\"menu-1-66c0f1d1\" class=\"elementor-nav-menu\"><li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-home menu-item-has-children menu-item-361\"><a href=\"https:\/\/bluter.at\/wp\/\" class=\"elementor-item\">H\u00e4mophilie<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3528\"><a href=\"https:\/\/bluter.at\/wp\/haemophilie-a-b\/\" class=\"elementor-sub-item\">H\u00e4mophilie A &#038; B<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2859\"><a href=\"https:\/\/bluter.at\/wp\/von-willebrand-syndrom\/\" class=\"elementor-sub-item\">Von-Willebrand-Syndrom<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2858\"><a href=\"https:\/\/bluter.at\/wp\/bluterinnen-konduktorinnen\/\" class=\"elementor-sub-item\">Bluterinnen &#038; Konduktorinnen<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-930\"><a href=\"https:\/\/bluter.at\/wp\/faq\/\" class=\"elementor-sub-item\">FAQ<\/a><\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4898\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\">\u00d6HG<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-4986\"><a href=\"https:\/\/bluter.at\/wp\/team\/\" class=\"elementor-sub-item\">Team<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2794\"><a href=\"https:\/\/bluter.at\/wp\/medizinischer-beirat\/\" class=\"elementor-sub-item\">Medizinischer Beirat<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-508\"><a href=\"https:\/\/bluter.at\/wp\/jahresbericht\/\" class=\"elementor-sub-item\">Jahresbericht<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2798\"><a href=\"https:\/\/bluter.at\/wp\/mitgliedschaft\/\" class=\"elementor-sub-item\">Mitgliedschaft<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2799\"><a href=\"https:\/\/bluter.at\/wp\/sponsoren-spenden\/\" class=\"elementor-sub-item\">Sponsoren &#038; Spenden<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2795\"><a href=\"https:\/\/bluter.at\/wp\/arbeitsschwerpunkte-projekte\/\" class=\"elementor-sub-item\">Arbeitsschwerpunkte &#038; Projekte<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2793\"><a href=\"https:\/\/bluter.at\/wp\/geschichte\/\" class=\"elementor-sub-item\">Geschichte<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-8024\"><a href=\"https:\/\/bluter.at\/wp\/statuten\/\" class=\"elementor-sub-item\">Statuten<\/a><\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-969\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\">Aktivit\u00e4ten<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4991\"><a href=\"#\" class=\"elementor-sub-item elementor-item-anchor\">Veranstaltungen<\/a>\n\t<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2852\"><a href=\"https:\/\/bluter.at\/wp\/wintertreffen\/\" class=\"elementor-sub-item\">Wintertreffen<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3471\"><a href=\"https:\/\/bluter.at\/wp\/stammtisch\/\" class=\"elementor-sub-item\">Stammtisch<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-4119\"><a href=\"https:\/\/bluter.at\/wp\/active-days\/\" class=\"elementor-sub-item\">Active Days<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3585\"><a href=\"https:\/\/bluter.at\/wp\/sommercamp\/\" class=\"elementor-sub-item\">Sommercamp<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3469\"><a href=\"https:\/\/bluter.at\/wp\/frauen-mutterwochenende\/\" class=\"elementor-sub-item\">Frauen- &#038; M\u00fctterwochenende<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5007\"><a href=\"https:\/\/bluter.at\/wp\/generalversammlung\/\" class=\"elementor-sub-item\">Generalversammlung<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-7214\"><a href=\"https:\/\/bluter.at\/wp\/patiententreffen\/\" class=\"elementor-sub-item\">Patiententreffen<\/a><\/li>\n\t<\/ul>\n<\/li>\n\t<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4992\"><a href=\"#\" class=\"elementor-sub-item elementor-item-anchor\">Programme\/Projekte<\/a>\n\t<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3470\"><a href=\"https:\/\/bluter.at\/wp\/haemofit\/\" class=\"elementor-sub-item\">H\u00e4mofit<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5008\"><a href=\"https:\/\/bluter.at\/wp\/hamojob\/\" class=\"elementor-sub-item\">H\u00e4mojob<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5010\"><a href=\"https:\/\/bluter.at\/wp\/notfallhilfe\/\" class=\"elementor-sub-item\">Notfallhilfe<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5011\"><a href=\"https:\/\/bluter.at\/wp\/osterr-hamophilie-register\/\" class=\"elementor-sub-item\">\u00d6sterr. H\u00e4mophilie Register<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5009\"><a href=\"https:\/\/bluter.at\/wp\/humanitaere-hilfe\/\" class=\"elementor-sub-item\">Humanit\u00e4re Hilfe<\/a><\/li>\n\t<\/ul>\n<\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-968\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\">Information<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2805\"><a href=\"https:\/\/bluter.at\/wp\/news\/\" class=\"elementor-sub-item\">News<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-924\"><a href=\"https:\/\/bluter.at\/wp\/faktor-magazin\/\" class=\"elementor-sub-item\">FAKTOR Magazin<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5015\"><a href=\"https:\/\/bluter.at\/wp\/videos-podcasts\/\" class=\"elementor-sub-item\">Videos &#038; Podcasts<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2837\"><a href=\"https:\/\/bluter.at\/wp\/bestellservice\/\" class=\"elementor-sub-item\">Bestellservice<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3990\"><a href=\"https:\/\/bluter.at\/wp\/downloads\/\" class=\"elementor-sub-item\">Downloads<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-1397\"><a href=\"https:\/\/bluter.at\/wp\/links\/\" class=\"elementor-sub-item\">Links<\/a><\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4993\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\">Kontakt<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-4987\"><a href=\"https:\/\/bluter.at\/wp\/kontakt\/\" class=\"elementor-sub-item\">\u00d6HG B\u00fcro<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2855\"><a href=\"https:\/\/bluter.at\/wp\/behandlungszentren\/\" class=\"elementor-sub-item\">Behandlungszentren<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3642\"><a href=\"https:\/\/bluter.at\/wp\/im-notfall\/\" class=\"elementor-sub-item\">Im Notfall<\/a><\/li>\n<\/ul>\n<\/li>\n<\/ul>\t\t\t<\/nav>\n\t\t\t\t\t<div class=\"elementor-menu-toggle\" role=\"button\" tabindex=\"0\" aria-label=\"Menu Toggle\" aria-expanded=\"false\">\n\t\t\t<i aria-hidden=\"true\" role=\"presentation\" class=\"elementor-menu-toggle__icon--open eicon-menu-bar\"><\/i><i aria-hidden=\"true\" role=\"presentation\" class=\"elementor-menu-toggle__icon--close eicon-close\"><\/i>\t\t\t<span class=\"elementor-screen-only\">Menu<\/span>\n\t\t<\/div>\n\t\t\t<nav class=\"elementor-nav-menu--dropdown elementor-nav-menu__container\" role=\"navigation\" aria-hidden=\"true\">\n\t\t\t\t<ul id=\"menu-2-66c0f1d1\" class=\"elementor-nav-menu\"><li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-home menu-item-has-children menu-item-361\"><a href=\"https:\/\/bluter.at\/wp\/\" class=\"elementor-item\" tabindex=\"-1\">H\u00e4mophilie<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3528\"><a href=\"https:\/\/bluter.at\/wp\/haemophilie-a-b\/\" class=\"elementor-sub-item\" tabindex=\"-1\">H\u00e4mophilie A &#038; B<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2859\"><a href=\"https:\/\/bluter.at\/wp\/von-willebrand-syndrom\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Von-Willebrand-Syndrom<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2858\"><a href=\"https:\/\/bluter.at\/wp\/bluterinnen-konduktorinnen\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Bluterinnen &#038; Konduktorinnen<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-930\"><a href=\"https:\/\/bluter.at\/wp\/faq\/\" class=\"elementor-sub-item\" tabindex=\"-1\">FAQ<\/a><\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4898\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\" tabindex=\"-1\">\u00d6HG<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-4986\"><a href=\"https:\/\/bluter.at\/wp\/team\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Team<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2794\"><a href=\"https:\/\/bluter.at\/wp\/medizinischer-beirat\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Medizinischer Beirat<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-508\"><a href=\"https:\/\/bluter.at\/wp\/jahresbericht\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Jahresbericht<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2798\"><a href=\"https:\/\/bluter.at\/wp\/mitgliedschaft\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Mitgliedschaft<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2799\"><a href=\"https:\/\/bluter.at\/wp\/sponsoren-spenden\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Sponsoren &#038; 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M\u00fctterwochenende<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5007\"><a href=\"https:\/\/bluter.at\/wp\/generalversammlung\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Generalversammlung<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-7214\"><a href=\"https:\/\/bluter.at\/wp\/patiententreffen\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Patiententreffen<\/a><\/li>\n\t<\/ul>\n<\/li>\n\t<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4992\"><a href=\"#\" class=\"elementor-sub-item elementor-item-anchor\" tabindex=\"-1\">Programme\/Projekte<\/a>\n\t<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3470\"><a href=\"https:\/\/bluter.at\/wp\/haemofit\/\" class=\"elementor-sub-item\" tabindex=\"-1\">H\u00e4mofit<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5008\"><a href=\"https:\/\/bluter.at\/wp\/hamojob\/\" class=\"elementor-sub-item\" tabindex=\"-1\">H\u00e4mojob<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5010\"><a href=\"https:\/\/bluter.at\/wp\/notfallhilfe\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Notfallhilfe<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5011\"><a href=\"https:\/\/bluter.at\/wp\/osterr-hamophilie-register\/\" class=\"elementor-sub-item\" tabindex=\"-1\">\u00d6sterr. H\u00e4mophilie Register<\/a><\/li>\n\t\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5009\"><a href=\"https:\/\/bluter.at\/wp\/humanitaere-hilfe\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Humanit\u00e4re Hilfe<\/a><\/li>\n\t<\/ul>\n<\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-968\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\" tabindex=\"-1\">Information<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2805\"><a href=\"https:\/\/bluter.at\/wp\/news\/\" class=\"elementor-sub-item\" tabindex=\"-1\">News<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-924\"><a href=\"https:\/\/bluter.at\/wp\/faktor-magazin\/\" class=\"elementor-sub-item\" tabindex=\"-1\">FAKTOR Magazin<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-5015\"><a href=\"https:\/\/bluter.at\/wp\/videos-podcasts\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Videos &#038; Podcasts<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2837\"><a href=\"https:\/\/bluter.at\/wp\/bestellservice\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Bestellservice<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3990\"><a href=\"https:\/\/bluter.at\/wp\/downloads\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Downloads<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-1397\"><a href=\"https:\/\/bluter.at\/wp\/links\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Links<\/a><\/li>\n<\/ul>\n<\/li>\n<li class=\"menu-item menu-item-type-custom menu-item-object-custom menu-item-has-children menu-item-4993\"><a href=\"#\" class=\"elementor-item elementor-item-anchor\" tabindex=\"-1\">Kontakt<\/a>\n<ul class=\"sub-menu elementor-nav-menu--dropdown\">\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-4987\"><a href=\"https:\/\/bluter.at\/wp\/kontakt\/\" class=\"elementor-sub-item\" tabindex=\"-1\">\u00d6HG B\u00fcro<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-2855\"><a href=\"https:\/\/bluter.at\/wp\/behandlungszentren\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Behandlungszentren<\/a><\/li>\n\t<li class=\"menu-item menu-item-type-post_type menu-item-object-page menu-item-3642\"><a href=\"https:\/\/bluter.at\/wp\/im-notfall\/\" class=\"elementor-sub-item\" tabindex=\"-1\">Im Notfall<\/a><\/li>\n<\/ul>\n<\/li>\n<\/ul>\t\t\t<\/nav>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-21dee502 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"21dee502\" data-element_type=\"section\">\n\t\t\t\t\t\t\t<div class=\"elementor-background-overlay\"><\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-5fb30fd6\" data-id=\"5fb30fd6\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-24fed086 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"24fed086\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-7397b05e\" data-id=\"7397b05e\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-6743a80a elementor-section-content-middle elementor-reverse-tablet elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"6743a80a\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-no\">\n\t\t\t\t\t<header class=\"elementor-column elementor-col-100 elementor-inner-column elementor-element elementor-element-516c604c\" data-id=\"516c604c\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-319e16d elementor-widget elementor-widget-text-editor\" data-id=\"319e16d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h1>von-Willebrand-Syndrom (VWS)<\/h1><p>Unter allen vererbten Blutgerinnungsst\u00f6rungen mit verl\u00e4ngerter Blutungszeit tritt das von-Willebrand-Syndrom am h\u00e4ufigsten auf. Rund 1% der Bev\u00f6lkerung ist davon betroffen. Je nach Schweregrad\/Typ der Erkrankung ist der sogenannte von-Willebrand-Faktor (VWF) vermindert (Typ 1 und 2), fehlt g\u00e4nzlich (Typ 3: VWF Restaktivit\u00e4t &lt;1%) und\/oder ist in seiner Qualit\u00e4t eingeschr\u00e4nkt (Typ 2). Da der VWF u.a. den Blutgerinnungsfaktor-VIII transportiert, ist auch dieser meist m\u00e4\u00dfig bis stark vermindert.<\/p><h2><em>Symptome<\/em><\/h2><p>Je nach Typ des VWS fallen die Symptome mehr oder weniger schwer aus: angefangen von einer erh\u00f6hten Neigung zu H\u00e4matomen und h\u00e4ufigem Nasenbluten, \u00fcber eine verl\u00e4ngerte Regelblutung bei Frauen, bis hin zu schweren Gelenkblutungen mit Folgesch\u00e4den. Die Blutungsneigung ist beim von-Willebrand-Syndrom meist schleimhautbetont. D.h. neben h\u00e4ufigem und verl\u00e4ngertem Nasenbluten k\u00f6nnen auch Zahnfleisch- und\/oder Gastrointestinalblutungen den Alltag beeintr\u00e4chtigen.<\/p><h2><em>Diagnose<\/em><\/h2><p>Die Diagnose des VWS wird labortechnisch gestellt. Dabei werden folgende Werte bestimmt:<\/p><ul><li>Gesamt-VWF-Antigen<\/li><li>VWF-Funktionspr\u00fcfung<\/li><li>Plasma-Faktor-VIII-Spiegel<\/li><li>aktivierte partielle Thromboplastinzeit (aPTT)<\/li><\/ul><p>Sind all diese Werte gleicherma\u00dfen um etwa 15-60% vermindert, spricht man vom Typ 1 VWS. Kann kein VWF-Antigen festgestellt werden und besteht ein deutlicher Faktor-VIII-Mangel, spricht man vom Typ 3. Im Vergleich zu diesen Formen besteht beim Typ 2 ein qualitativer Mangel, der sich durch eine verminderte Konzentration an VWF-Multimeren \u00e4u\u00dfert. Je nach funktioneller Ver\u00e4nderung des Faktors unterscheidet man beim Typ 2 wiederum vier Subtypen (2A, 2B, 2M, 2N).<\/p><p>\u00a0<\/p><h2><em>Behandlung\/Therapie<\/em><\/h2><h2>Tranexams\u00e4ure (Cyklokapron\u00ae)<\/h2><p>Dieser Wirkstoff sorgt daf\u00fcr, dass das gebildete Blutgerinnsel langsamer als gew\u00f6hnlich abgebaut wird, was zu einer verbesserten Festigkeit des gebildeten Thrombus f\u00fchrt. Daraus l\u00e4sst sich schlie\u00dfen, dass f\u00fcr die Wirkung des Medikaments noch Restaktivit\u00e4t der Gerinnung bestehen muss. Angewandt wird es demnach bei milderen Typen, meist in Tablettenform f\u00fcr Schleimhautblutungen.<\/p><p>\u00a0<\/p><h2>Desmopressin (DDAVP)<\/h2><p>Dieses Medikament erh\u00e4lt man f\u00fcr zu Hause meist als praktischen Nasenspray. Die Wirkung beruht u.a. auf der Aussch\u00fcttung von gespeichertem von-Willebrand-Faktor, wodurch man kurzzeitig einen erh\u00f6hten Spiegel und somit eine schnellere Blutgerinnung erzielt (max. Wert nach etwa 50 min). Es eignet sich deshalb gut als Prophylaxe vor dem Sport oder bei kleineren medizinischen Eingriffen (z.B. Zahnarztbesuch).<\/p><p>\u00a0<\/p><h2>Faktorkonzentrate<\/h2><p>Ist kaum eine Restaktivit\u00e4t mehr vorhanden (Typ 3, 2B), ist es notwendig den fehlenden Faktor mittels Kurzinfusion zuzuf\u00fchren. Daf\u00fcr stehen verschiedene Faktorkonzentrate zur Verf\u00fcgung, die alle zwei bis drei Tage \u00fcber die Venen verabreicht werden m\u00fcssen.<\/p><h2><em>\u00a0<\/em><\/h2><h2><em>Genetik &amp; Vererbung<\/em><\/h2><p>Vererbt wird das von-Willebrand-Syndrom unabh\u00e4ngig von den Geschlechtschromosomen (=autosomaler Erbgang). Das bedeutet, dass sowohl Frauen als auch M\u00e4nner betroffen sein k\u00f6nnen. W\u00e4hrend beim Typ 1 nur eine Erbanlage fehlerhaft sein muss, damit die Krankheit ausbricht, m\u00fcssen bei den schweren Formen beide Genanlagen defekt sein. Das ist der Grund, warum das VWS in seiner leichten Form (60-80% der Diagnosen) h\u00e4ufiger und in den schweren Formen nur sehr selten auftritt.<\/p><p>\u00a0<\/p><p>Literatur:<\/p><ul><li>Schneppenheim R.\/ Budde U. (2010): von Willebrand-Syndrom und von Willebrand-Faktor: aktuelle Aspekte der Diagnostik und Therapie. Bremen: UNI-MED-Verlag 3. Auflage<\/li><li>Kurnik K.\/ Von Depka Prondzinski M. (2009): Von-Willebrand-Syndrom. Ein Leitfaden f\u00fcr Patienten. Stuttgart: TRIAS Verlag<\/li><li>Goodeve A.\/James P. (2014): von Willebrand Disease, Online unter: <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK7014\/\">https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK7014\/<\/a><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/header>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2714a7ce elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2714a7ce\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-626c4263\" data-id=\"626c4263\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element 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srcset=\"https:\/\/bluter.at\/wp\/wp-content\/uploads\/2023\/04\/Welthaemophilietag-2023-640x372.jpg 640w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2023\/04\/Welthaemophilietag-2023-1280x745.jpg 1280w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2023\/04\/Welthaemophilietag-2023-1024x596.jpg 1024w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2023\/04\/Welthaemophilietag-2023-1536x894.jpg 1536w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2023\/04\/Welthaemophilietag-2023-1200x700.jpg 1200w, https:\/\/bluter.at\/wp\/wp-content\/uploads\/2023\/04\/Welthaemophilietag-2023.jpg 1586w\" sizes=\"(max-width: 640px) 100vw, 640px\" \/><\/div>\n\t\t<\/a>\n\t\t\t\t<div class=\"elementor-post__text\">\n\t\t\t\t<\/div>\n\t\t\t\t<\/article>\n\t\t\t\t<\/div>\n\n\n\t\t\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3c767a1b elementor-button-info elementor-align-center elementor-widget elementor-widget-button\" data-id=\"3c767a1b\" 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elementor-element-65018825 elementor-widget elementor-widget-image\" data-id=\"65018825\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<a href=\"https:\/\/www.osgs.at\/oesterreichische-haemophilie-gesellschaft-oehg\" target=\"_blank\">\n\t\t\t\t\t\t\t<img decoding=\"async\" src=\"https:\/\/bluter.at\/wp\/wp-content\/uploads\/elementor\/thumbs\/spende-p31fltilxpojyvy2xw9hn1yn8lphdgkdbxw7lz9tk8.png\" title=\"spende\" alt=\"spende\" loading=\"lazy\" \/>\t\t\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-20 elementor-top-column elementor-element elementor-element-690bb4 elementor-invisible\" data-id=\"690bb4\" data-element_type=\"column\" data-settings=\"{&quot;animation&quot;:&quot;fadeIn&quot;,&quot;animation_delay&quot;:100}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1749130d elementor-widget elementor-widget-heading\" data-id=\"1749130d\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Adresse<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-ca917c3 elementor-icon-list--layout-traditional elementor-list-item-link-full_width elementor-widget elementor-widget-icon-list\" data-id=\"ca917c3\" data-element_type=\"widget\" data-widget_type=\"icon-list.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<ul class=\"elementor-icon-list-items\">\n\t\t\t\t\t\t\t<li class=\"elementor-icon-list-item\">\n\t\t\t\t\t\t\t\t\t\t\t<a href=\"https:\/\/www.google.com\/maps\/place\/Mariahilfer+G%C3%BCrtel+4,+1060+Wien,+%C3%96sterreich\/@48.19114,16.338215,15z\/data=!4m5!3m4!1s0x476da81f6bd38a73:0xff57fbe69b6fc254!8m2!3d48.1911401!4d16.3382148?hl=de-DE\" target=\"_blank\">\n\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-icon-list-icon\">\n\t\t\t\t\t\t\t<i aria-hidden=\"true\" class=\"fas fa-map-marker-alt\"><\/i>\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-icon-list-text\">Mariahilfer G\u00fcrtel 4, 1060 Wien<\/span>\n\t\t\t\t\t\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t\t\t\t<\/li>\n\t\t\t\t\t\t\t\t<li class=\"elementor-icon-list-item\">\n\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-icon-list-icon\">\n\t\t\t\t\t\t\t<i aria-hidden=\"true\" class=\"fas fa-phone\"><\/i>\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-icon-list-text\">+43 664 18 69 804<\/span>\n\t\t\t\t\t\t\t\t\t<\/li>\n\t\t\t\t\t\t\t\t<li class=\"elementor-icon-list-item\">\n\t\t\t\t\t\t\t\t\t\t\t<span 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